Total anomalous pulmonary venous connection

Also known as: 전폐정맥연결 이상 총폐정맥 환류 이상증, 총폐정맥이상연결증

Neurosurgery doctors

Doctors who treat Total anomalous pulmonary venous connection

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Eunpyeong St. Mary's Hospital, Catholic University of Korea Kim Beom-jun

Kim Beom-jun

Eunpyeong St. Mary's Hospital, Catholic University of Korea · Pediatrics

선천성심질환, 심잡음, 가와사끼병, 흉통, 실신, 부정맥, 심근증, 고혈압, 폐동맥고혈압

Changwon Gyeongsang National University Hospital Kim Jong-u

Kim Jong-u

Changwon Gyeongsang National University Hospital · Thoracic and Cardiovascular Surgery

성인심장(심장판막질환, 관상동맥질환, 대동맥질환, 심장이식, 선천성 심장질환), 혈관외과 (대동맥스텐트 시술, 말초혈관질환), 소아심장(단순 선천성 기형), 소아흉부외과

Seoul St. Mary's Hospital, Catholic University of Korea Lee Cheol

Lee Cheol

Seoul St. Mary's Hospital, Catholic University of Korea · Thoracic and Cardiovascular Surgery

소아 심장외과,소아 선천성심장병,성인 선천성 심장병

Seoul St. Mary's Hospital, Catholic University of Korea Lee Won-yeong

Lee Won-yeong

Seoul St. Mary's Hospital, Catholic University of Korea · Thoracic and Cardiovascular Surgery

소아 선천성 심질환 성인 선천성 심질환

St. Vincent's Hospital, Catholic University of Korea Cho Deok-gon

Cho Deok-gon

St. Vincent's Hospital, Catholic University of Korea · Thoracic and Cardiovascular Surgery

흉부종양(폐암,식도암, 흉선종), 다한증, 로봇수술 및 흉강경수술, 소아흉부질환, 외상외과

St. Vincent's Hospital, Catholic University of Korea Hyun Gwan-yong

Hyun Gwan-yong

St. Vincent's Hospital, Catholic University of Korea · Thoracic and Cardiovascular Surgery

흉부종양(폐암,식도암,흉선종), 로봇수술, 홍조/다한증, 오목가슴/새가슴, 소아흉부질환

Ajou University Hospital Hong Yu-seon

Hong Yu-seon

Ajou University Hospital · Thoracic and Cardiovascular Surgery

심부정맥혈전증

Ajou University Hospital Yoo U-sik

Yoo U-sik

Ajou University Hospital · Thoracic and Cardiovascular Surgery

폐암, 식도암, 종격동 종양, 로봇수술, 폐이식

Yonsei University Severance Hospital Kim Ha-eun

Kim Ha-eun

Yonsei University Severance Hospital · Thoracic and Cardiovascular Surgery

폐암,폐이식,간질성 폐질환,소아흉부질환,종격동 종양(로봇수술),전이성 폐질환

Yonsei University Severance Hospital Yang Yeong-ho

Yang Yeong-ho

Yonsei University Severance Hospital · Thoracic and Cardiovascular Surgery

흉선암(로봇,단일공 수술),폐암,식도암,폐이식,간유리 음영 결절,기관 및 기관지 질환,소아 흉부 질환

Disease Description (Causes and Symptoms)

Ileus is a condition in which the small or large intestine is partially or completely obstructed, preventing the passage of intestinal contents (food, digestive juices, and gas), thereby causing increased intestinal pressure, intestinal distension, and impaired digestion and absorption.
Main causes

  • Mechanical obstruction: postoperative adhesions, tumors (small intestine cancer·colorectal cancer), incarceration due to a hernia, intussusception, volvulus, etc.
  • Paralytic (functional) obstruction: decreased intestinal motility due to peritonitis, acute pancreatitis·cholecystitis, abdominal trauma·immediately after surgery, certain medications (analgesics·anticholinergics, etc.), etc.
    Summary of pathophysiology
  • Intestinal contents accumulate above the site of obstruction, causing distension·pain·vomiting → increased intraluminal pressure reduces blood flow → increased risk of intestinal mucosal ischemia·necrosis·perforation and sepsis
    Main symptoms
  • Intermittent (paroxysmal) abdominal pain (cramping), abdominal distension, vomiting (severe and bilious in upper small-intestine obstruction; feculent vomiting may occur as time passes), cessation of bowel movements·gas passage (in complete obstruction), dehydration·tachycardia·hypotension, fever·increased white blood cell count (in cases of necrosis·perforation·infection)
    Physical examination findings
  • Early mechanical obstruction: hyperactive bowel sounds (high-pitched bowel sounds)
  • Paralytic ileus or advanced condition: decreased or absent bowel sounds

Treatment Methods (Standard Treatment·Medications·Procedures/Surgery·Lifestyle Management and Precautions)

Initial management (emergency·primary)

  • Nothing by mouth (NPO), intravenous fluids (fluid·electrolyte correction), correction of electrolyte·acid-base status
  • Gastrointestinal decompression: aspiration of gastric contents (decompression) by inserting a nasogastric tube (Levin or nasogastric tube)
  • Control of pain·vomiting (antiemetics and analgesics as needed—use carefully so as not to mask diagnostic signs), broad-spectrum antibiotics if necessary (when perforation·peritonitis is suspected)
    Diagnostic tests
  • Upright plain abdominal X-ray: suspected intestinal obstruction based on observation of air-fluid levels
  • Contrast-enhanced abdominal CT: most useful for identifying the site of obstruction·transition point·intestinal ischemia·cause (tumor·hernia, etc.)
  • Blood tests: CBC, electrolytes, renal function, blood gas·lactate — important when intestinal ischemia is suspected
    Criteria for conservative (nonoperative) treatment
  • If there is partial obstruction, no evidence of necrosis·perforation·peritonitis, and symptoms improve with decompression·fluid therapy, observation and continued conservative management may be appropriate
    Indications for surgery
  • Emergency surgery is indicated for complete obstruction, evidence of intestinal ischemia·necrosis·perforation or peritonitis, failure of conservative treatment, progressive shock, or rapid worsening of symptoms
    Examples of surgical treatment
  • Adhesiolysis, resection of necrotic intestine followed by anastomosis or stoma formation, hernia repair·correction, reduction of intussusception in children with an air·barium enema, and, in some cases, endoscopic stent placement for malignant colorectal obstruction
    Follow-up·lifestyle management and precautions
  • When symptoms improve after fasting, gradually resume oral intake (clear liquids → semi-liquid diet → regular diet)
  • Carefully correct dehydration·electrolyte abnormalities and monitor bowel movements·gas passage
  • Analgesics (especially opioids) may suppress intestinal motility, so discuss their necessity and dosage with a doctor
  • Early medical evaluation is recommended if there is a history of abdominal surgery (risk of adhesions) or signs of a hernia
    Risk of complications
  • Intestinal ischemia·necrosis, perforation, peritonitis, sepsis, electrolyte abnormalities·shock

Checklist Before an Outpatient Visit (Including Items to Bring and Example Questions)

Items to bring

  • List of medications currently being taken (name·dose·time of administration) and recent prescriptions
  • Past medical history·surgical records (especially abdominal surgery·hernia·history of cancer)
  • Films or a CD of recent test results or imaging (abdominal X-ray/CT, etc.), and test reports
  • Onset and course of symptoms (specific timing·frequency·volume), and a photo or record of vomit (if available)
  • Recent weight changes, time of the last bowel movement·gas passage, presence of fever, and whether urine output has decreased
    Useful items to record for the outpatient visit
  • Characteristics of pain (paroxysmal·continuous), number of vomiting episodes and contents (bilious·feculent), degree of abdominal distension, and changes in meals·medications
    Restrictions/precautions before the visit
  • Visit while fasting (if instructed by a doctor), and avoid consuming food orally without a prescription or instructions
    Examples of simple questions to ask at an outpatient visit (to prepare for asking the doctor)
  • “I have a history of abdominal surgery. How likely is it that these symptoms are caused by adhesions?”
  • “What are the criteria for determining whether hospitalization·surgery is needed in my current condition?”

General Example Questions to Ask the Doctor

  • “Given my current condition, how likely is it that I will improve with conservative treatment (decompression·fluid therapy)?”
  • “If surgery is necessary, what type of surgery is expected, and what is the risk of complications?”
  • “Besides fluid·electrolyte correction, is there anything I can do at home to manage my condition?”
  • “What should I avoid in terms of lifestyle (diet·medications·activity) during or after treatment?”

Disease-Specific Example Questions

  • “I have had abdominal surgery in the past (or repeated intestinal surgery). Are there specific ways to prevent recurrent adhesive intestinal obstruction?”
  • “A localized transition point was observed on my abdominal CT. In this case, is nonsurgical treatment (such as an endoscopic stent) possible, and what are the indications for surgery? Please explain.”

(Note: The above information summarizes general diagnostic·treatment guidelines. Because testing·treatment plans may vary depending on the individual patient’s condition, be sure to consult the treating medical professionals.)

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This information is for general understanding only and does not replace diagnosis, prescription or treatment for an individual patient. If you have symptoms, please see a doctor.

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